 |
|
|
|
TEST-CHAPTER ELEVEN
Questions marked
with * are more appropriate
for residents.CNS MALFORMATIONS
1. Exposure to a teratogen may cause CNS malformations if it occurs at 3 to 8
weeks of gestation and have minimal or no effects if it occurs later
2. Congenital CMV infection at 9-12 weeks of gestation can cause:
3. Congenital CMV infection starting at 37 weeks gestation can cause:
4. To be effective in preventing neural tube defects, women of child-bearing
age must take 0.8 mg folic acid daily:
5. Which is not a neural tube defect
6. Mutation of which is associated with NTDs?
*7. Which of the following mutations is associated
with NTDs?
9. HPE may be associated with all of the following except:
10. HPE may be associated with all of the following except:
*11. A newborn baby with a single central incisor may
have:
12. Which of the following is implicated in the pathogenesis of HPE?
13. Agenesis of the corpus callosum may be confused in fetal ultrasound with alobar HPE
14. Patients with agenesis of the corpus callosum may have relatively normal intelligence
15. The most common chromosomal abnormality associated with HPE is:
16. Lissencephaly is most commonly associated with:
17. Which of the following is associated with abnormal cortical layering:
*18. Abnormal neuronal migration may cause:
*19. A smooth cortex and large ventricles on fetal
ultrasound without other abnormalities is most likely
caused by:
20. A microdeletion of 17p may be associated with:
21. A thick cortex with abnormal neuronal layering is seen in:
22. Lissencephaly may be associated with all of the following except:
23. Hydrocephalus ex vacuo is seen in all of the following conditions except:
24. The most common cause of obstructive hydrocephalus in children is:
25. The Chiari I malformation shows all of the following except:
26. The key feature of the Dandy-Walker Syndrome is:
27. Patients with the Chiari II malformation may have all of the following except:
28. The picture below shows the spinal cord in the
center. A portion of a vertebral body is seen
anterior to it. The illustrated pathology may be associated
with all of the following
except:
*29. The picture below shows the cerebellum viewed
from behind and above. The illustrated pathology is:
30. The illustrated pathology is invariably associated with severe psychomotor
retardation 
31. The illustrated pathology is associated with:
32. The pathology in a newborn infant depicted below
is associated with:
33. The pathology depicted is associated with all of the following except:
*34. The illustrated lesion may be associated with
all of the following except:
 |